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Title: PSEUDOMYXOMA PERITONEI - A RARE CASE REPORT
e-poster Number: EP 173
Category: Gynaecologic Oncology
Author Name: Dr. Jigyasa Sharma
Institute: Ananta institute of medical sciences rajsamand
Co-Author Name:
Abstract :
A 33 year old female multigravida came with chief complaint of mass protruding out per vaginally since 1 year , on examination an abdomino -pelvic mass with 3rd degree utero-vaginal prolapse with grade 3 cystocele and rectocele was diagnosed. Ultrasonography of whole abdomen and pelvis suggested a large cystic lesion with internal septations and echoes further extending into perihepatic and perihilar spaces suggesting mucinous cystic neoplasm originating from the ovary . CECT on further evaluation suggested pseudomyxoma peritonei .The patient underwent a complete cytoreductive surgery with total abdominal hysterectomy with bilateral salpingo-oopherectomy with Infracolic omentectomy with appendicectomy followed by removal of as much as mucin deposits as possible . Intraoperative frozen section sent intraoperatively favoured low grade mucinous cystadenoma of the left ovary. Final histopathological examination of the specimen confirmed borderline left ovarian mucinous tumor and ruptured mucocele of the appendix. The patient withstood the procedure well. The pelvic anatomy with lot of adhesions proved to be surgical challenges while performing the procedure. Pseudomyxoma Peritonei (PMP) also known as ?jelly belly? is a rare case with an incidence of approximately 1 in a million annually. It usually arises from mucocele of the appendix and less commonly from the ovary. Early diagnosis is difficult as it runs a very indolent course leading to many patients presenting at advanced stages of the disease condition marked by diffuse mucinous implants on the peritoneal surfaces. The 'redistribution phenomenon' explains how intraperitoneal fluid, aided by gravity, helps free-floating mucinous tumor cells implant in different parts of the peritoneal cavity. The small bowel is often spared due to its peristaltic movements. Diagnosis is challenging, and most cases are discovered incidentally through imaging. Due to its rarity, there is no standardized treatment approach for pseudomyxoma peritonei.